Case report Heryln - Werner - Wunderlich Syndrome
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چکیده
Herlyn – Werner – Wunderlich syndrome (HWWS) is an uncommon combined Mullerian and Mesonephric duct anomaly, and its presentation in neonatal period is even rarer. Symptoms generally occur after menarche about 12 to 13 years old and it is usually diagnosed by pelvic magnetic resonance imaging. Our case is 1 day old asymptomatic newborn with all the features of this syndrome that came to our attention during diagnostic workup of rectovesical fistula and meningomyelocele. The aim of this article is to share our experience of coincidental association of this syndrome along with other malformations and focus the attention on the importance of high level of suspicion of HWWS in neonatal period which leads to early diagnosis and treatment.
منابع مشابه
Herlyn Werner Wunderlich Syndrome with Hematocolpos: An Unusual Case Report of Full Diagnostic Approach and Treatment
Herlyn-Werner-Wunderlich (HWW) syndrome is an uncommon combined müllerian duct anomalies (MDAs) and mesonephric duct malformation of female urogenital tract characterized by uterus didelphys and obstructed hemi-vagina and ipsilateral renal agenesis (OHVIRA) syndrome. We present a rare and unusual case of this syndrome in a 19 year-old female who suffered from hypomenorrhoea and abdominal pain. ...
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Uterine didelphys with obstructed hemivagina and ipsilateral renal agenesis is a rare congenital anomaly of the Müllerian duct system referred to as Herlyn-Werner-Wunderlich syndrome. Because of its rare occurrence, a high level of suspicion is often required for diagnosis. Clinically, these patients usually present after menarche with pelvic pain, dysmenorrhea, and a palpable pelvic mass. We p...
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Herlyn-Werner-Wunderlich (HWW) syndrome is a very rare congenital anomaly of the urogenital tract resulting from maldevelopment of both Mullerian and Wolffian ducts. It is characterized by the triad of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis. It generally presents at puberty shortly following menarche with the symptom of acute pelvic pain. Management of these case...
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